ANAESTHETIC MANAGEMENT OF A PATIENT WITH HUNTINGTON’S CHOREA - A CASE REPORT
Dr. Akansha Singh, Dr. Shweta Mahajan*, Dr. Cliffin Mathai Kattoor, Dr. Abhinav Kumar and
Dr. Jyotsna Guleria
Huntington's disease is a rare dominantly inherited progressive autosomal disease affecting the basal ganglia. The disease manifests later in life as progressive mental deterioration causing personality change and involuntary choreiform movements. The most ominous motor symptom, dysphagia, hinders nutritional intake and places the patient at an increased risk of aspiration. The real challenge for an anaesthetist in the management of a patient with Huntington’s chorea lies in treating the frail elderly uncooperative patient, treating the patients suffering from malnutrition and dealing with increased risk of aspiration and exaggerated response to Succinylcholine and Thiopentone in these patients. We report the anesthetic management of a 62-year-old female patient with Huntington's chorea admitted for an elective orthopedic procedure.
Keywords: Huntington's disease; Basal ganglia; Involuntary choreiform movements; Autosomal; Personality change; GABA.
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