RARE CASE OF STURGE WEBER SYNDROME DIAGNOSED ON NCCT HEAD

Dr. Malvika Shitak* and Dr. Ishan Sharma

ABSTRACT

Sturge-Weber syndrome is a syndrome of unknown etiology that is characterized by port wine vascular nevus flammeus in the trigeminal nerve distribution, leptomeningeal venous angiomatosis and they presents with seizures, dementia and hemiplegia. In patients with Sturge-Weber syndrome, X-ray findings in the skull usually show a tram-track pattern of calcification that is caused by calcification in opposing gyri on either side of an intervening dilated sulcus. On CT, curvilinear calcifications in a gyral pattern are often seen, primarily in the occipital and posterior parietal lobes ipsilateral to the facial angioma.

Keywords: Portwine stain, gyral calcifications, cortical atrophy.