CAUSAL LINK BETWEEN BUDD-CHIARI SYNDROME AND POLYCYTHEMIA VAQUEZ: CASE REPORT AND REVIEW OF THE LITERATURE
S. Bouchrit*, S. Boudda, Y. Lemfadli, A. Ait Errami, S. Oubaha, Z. Samlani and K. Krati
The aetiologies of Budd-chiari syndrome are multiple dominated by myeloproliferative syndromes, present in 50% of carriers of primary SBC. Myeloproliferative syndromes group together several pathologies, namely polycythemia vera, essential thrombocythemia and myelofibrosis. The PV is the entity most frequently associated with a primitive SBC. The blood count abnormalities are often masked by portal hypertension in splanchnic thrombosis. The diagnosis of polycythemia vera is based on BMB and the therapeutic management must be multidisciplinary using hematology, gastroenterology and cardiology in order to manage anticoagulants on the one hand and the complications of portal hypertension on the other hand.
Keywords: Budd-Chiari syndrome, myeloproliferative syndrome, polycythemia vera.
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