ULNAR ADAMANTINOMA - A RARE TUMOUR AT A RARE SITE

Dr. Maymol P. Varghese, MBBS*, Dr. Lekha K. Nair, MD, Dr. Joy Augustine, MD, DCP and Dr. Dominic K. Puthoor, MS, D. Ortho

ABSTRACT

Background: Adamantinoma is a rare slow growing tumour with malignant potential. Males of 20-50 years are usually affected. This neoplasm has a predilection for tibia and upper extremity involvement is very rare. Case Presentation: A 24 year old male patient presented with a swelling in the left forearm. X-ray showed a lytic lesion in the mid-shaft of ulna. Imprint cytology revealed a spindle cell lesion. Curettage and biopsy was done. Microscopy revealed a spindle cell neoplasm arranged in storiform pattern showing positivity for CK and vimentin with immunohistochemistry. Conclusion: Our histopathological and immunohistochemical features were suggestive of Adamantinoma. The case is unusual because of the rarity of the tumour and even rare occurrence of the neoplasm in upper limb. Hence adamantinoma should be considered in differentials of lytic lesion of the upper limb even though the predilection for these sites are rare.

Keywords: Adamantinoma, Ulna, Lytic lesion.