ACUTE FEBRILE NEUTROPHILIC DERMATOSIS (SWEET SYNDROME) - A RARE CASE REPORT WITH LITERATURE REVIEW
Sonali Maria Vas* and Sheethal Kuriakose
ABSTRACT
Introduction: Sweet syndrome is a rare skin disorder of unknown etiology. It is characterized by fever and the sudden onset of a rash. The typical age of onset is between 30 and 60 years of age, although cases have been reported in the paediatric and elderly populations as well. Case presentation: This study presents a case of an 8 year old male patient who had a seven day history of fever, lesions over the skin and redness in both eyes. She also presented with mouth ulcers in the last 4 days. Cultures, a biopsy and laboratory tests yielded a diagnosis of sweet syndrome. The case was managed successfully by pharmacotherapy and was resolved within 2 months. Discussion: Sweet syndrome is a very rare inflammatory skin disorder in children and has only 80 reported cases in the medical literature. Diagnosis primarily depends on histopathological examination. Treatment with corticosteroids is considered the ideal choice for such pathology. Conclusion: This case is exceptional because the occurrence of sweet syndrome in children is extremely rare and accurate diagnosis is necessary to initiate effective treatment. Its head, neck and oral manifestations and its association with paraneoplastic disease warrant the need to be aware of the condition.
Keywords: paraneoplastic, autoimmune, idiopathic, bullous pyoderma, gangrenosum.
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