HLH SYNDROME – UNCOMMON ENTITY WITH OVERLAP PRESENTATION. A CASE REPORT
*Dr. Syed Fahimuddin, Dr. Wasim Shabbir Shaikh, Dr. Mohammed Nayeem, Dr. Bipin Panchpande, Dr. Zeyad Alrais, Mohammed Baqer, Dr. Rania Medhat Seleim
Hemophagocytic lymphohistiocytosis (HLH), is an uncommon hematologic disorder seen more often in children than in adults. It is a life-threatening disease of severe inflammation caused by uncontrolled rapid increase of activated lymphocytes and macrophages, leading to cytokine storm syndromes. There are inherited and non- inherited (acquired) causes of hemophagocytic lymphohistiocytosis (HLH) (we can omit this line). We report an unusual presentation of HLH and it’s management in a previously healthy gravid lady.
Keywords: Hlh, Cytokine Storm, Etoposide, Steroid, Rituximab.
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