CASE REPORT OF AN EXTRALOBAR SEQUESTRATION HYBRID LUNG LESION ASSOCIATED WITH TWO CYSTIC PULMONARY AIRWAY MALFORMATIONS IN THE IPSILATERAL LEFT HEMITHORAX

Érika Mailaro Jordão; Fabricio Nunes Zacca MD; Anna Carolina Chiorino Lopez Poloni MD; Beatriz Durante Pasin MD; Leonan Tavares Galvão MD, Mauricio Giusti Calderon MD, MsC*

ABSTRACT

Extralobar sequestration is a rare congenital anomaly characterized by a mass of pulmonary parenchyma with it is own pleura, lacking communication with the tracheobronchial tree, with a blood supply from descending aorta and varied venous drainage. In this case we report the association of a congenital cystic adenomatoid malformation, a lesion that communicates with the tracheobronchial tree and has a direct arterial supply to the pulmonary circulation. The risk factors and etiology are not completely elucidated, and the scarcity of reports about the occurrence of both of these pathologies makes the rarity of the case even greater and demonstrates the relevance of this study. We describe a case of ipsilateral left hemithorax lesions in a newborn patient who was diagnosed prenatally by a 32-week ultrasound. Early surgical intervention on the ninth day after birth instituted an effective operative excision with curative intention to treat.

Keywords: Extralobar sequestration, case report, congenital cystic adenomatoid malformation, left hemithorax.