PEUTZ-JEGHERS SYNDROME: ABOUT A NEW CASE REPORT
M. A. Lkousse*, K. Gharbi, A. Elfarouki, S. Roudi, A. Aiterrami, S. Oubaha and Z. Samlani and K. Krati
Peutz-Jeghers syndrome (PJS) is an unusual gastrointestinal hamartomatous polyposis, inherited in an autosomal dominant pattern, defined by the association of periorificial lentiginosis with gastrointestinal, pulmonary and reproductive organs involvement. The case of a 18 years old man with an intussusception is reported. A polyp was proved to be the cause of the intussusception. Histologically, it was a hamartoma. Most of these patients have recurrent episodes of intussusception caused by polyps, with an increased risk of malignant disease, and require endoscopic screening and regular periodic monitoring.
Keywords: Peutz-Jeghers, polyposis, hamartoma, lentiginosis, periodic monitoring.
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