IVEMARK SYNDROME IN A NEONATE- CASE REPORT

*Dr. Sachin Dangi and Namita Gwasikoti

ABSTRACT

Ivemark syndrome is an uncommon congenital disorder which is characterized by involvement of multiple organ systems. Patients with this condition may have cardiac malformations, hypoplasia or aplasia of the spleen and the abnormal anatomy of abdominal and thoracic viscera. It is often associated with severe cardiac abnormalities, which are the usual causes of death in early neonatal life. To our knowledge only a few cases of Ivermark syndrome has been described in Indian literature. Here we report a case of a neonate who was diagnosed as Ivemark syndrome.

Keywords: Ivemark syndrome, Asplenia syndrome, Heterotaxy disorders.