DESMOID FIBROMA OF SOFT TISSUES OF EXTRA-ABDOMINAL SITE: ABOUT A CASE AND REVIEW OF THE LITERATURE

Taghzout Hasnae*, Hafidi Khaoula, Abboud Fatima Zahrae, Alami Zineb, Bouhafa Touria and Hassouni
Khalid

ABSTRACT

Extra-abdominal desmoid fibromatosis (EADF) is a rare benign tumor with a high risk of local recurrence, which distinguishes it from other benign tumors.This tumor mainly affects women in the third and fourth decades. The pathogenesis of these extra-abdominal tumors remains unknown. MRI (Magnetic resonance imaging) is most useful for the diagnosis and follow-up of a desmoid tumor. Anatomopathological examination confirms the diagnosis of this tumor, which raises a problem of differential diagnosis with low-grade fibrosarcomas. Surgery remains the main part of the therapeutic protocol despite the appearance of new means such as radiotherapy and hormone therapy. We report a case of extra abdominal desmoid tumor treated essentially by surgery with adjuvant radiotherapy without any sign of recurrence.

Keywords: Desmoid Tumours, Fibrosarcomas, Recidivism, Surgery, Radiotherapy, Hormone Therapy.