“A SICKLE CELL TRAIT CHILD WITH A SEQUELA -MOYAMOYA SYNDROME”

*Dr. Gaurav Agarwal, Dr. Monica Lazarus and Dr. Manish Ajmariya

ABSTRACT

Moyamoya Syndrome is a chronic cerebrovascular disorder characterized by progressive steno-occlusion of cerebrovascular arteries leading to development of collaterals network at the base of brain. It has been seen as an uncommon neurological complication of few haemoglobinopathies including sickle cell disease, however only three such cases of moyamoya syndrome with sickle cell trait have been reported in the literature. We report a 6 yr. old female child, who presented to hospital with headache and vomiting, subsequently developed sudden loss of vision and symptoms of neurological dysfunction diagnosed as moyamoya syndrome associated with her known sickle cell trait etiology.

Keywords: headache, sickle cell trait, moyamoya syndrome.