VEIN OF GALEN MALFORMATION- A RARE LIFE-THREATENING DISEASE

A. Pandey* and S. Badole

ABSTRACT

The scope of this review article is to provide information on vein of galen malformation. Vein of Galen aneurysmal malformation (VGAM) is a rare but potentially life-threatening cerebral vascular malformation with an estimated incidence of 1 in 25,000. VGAM represents nearly 30% of all pediatric cerebrovascular malformations. Survival rate is very low in the cases of this disease. In the more severe cases, the blood overload goes almost directly from the vein to the heart and rapidly overwhelms it, leading to congestive heart failure. VGM is a rare life-threatening disease and even after surgical treatment, the mortality rate remains as high as 39.4%. This article also highlights latest cases on VGM and their life expectancy.

Keywords: VGAM, aneurysm, heart failure, blood.